Long‐Term Outcomes in Patients With Connective Tissue Disease–Associated Pulmonary Arterial Hypertension in the Modern Treatment Era: Meta‐Analyses of Randomized, Controlled Trials and Observational Registries

Meta-analysis (11 RCTs [n=4,329; 1,267 with CTD‐PAH] & 19 registries [n=9,739; 4,008 with CTD‐PAH]) found modern therapy provides similar reduction in morbidity/mortality risk (36%) in patients with CTD‐PAH vs PAH population overall.

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Arthritis and Musculoskeletal Alliance